Isifo Rasmussen sika (encephalitis). Izizathu Rasmussen syndrome

isifo Rasmussen sika kungokwalabo esigabeni izifo ezingavamile ukuvuvukala oluqubuka empandleni ingqondo. Lokhu encephalitis ngokuvamile kwenzeka ezinganeni ezingaphansi kweminyaka engu-15. Ngokuvamile, ukugula sitholakale ubudala. Ngo intsha kanye nabantu abadala, lolu hlobo encephalitis ivelakancane.

Le nqubo ihlanganisa omunye Nenkabazwe zobuchopho. Njengoba isifo siqhubeka, odokotela wakuphawula yoma ezithuthukayo. Odokotela ukhombe ukumelana kakhulu zokwelapha isifo. Empeleni, lesi sifo Rasmussen - encephalitis izici eziqondile ngeke welaphe.

izimbangela kungenzeka encephalitis Rasmussen

Kuze kube etiology lesi sifo engakaze isungulwe. Ososayensi amchaze kuphela izici ezintathu eziyinhloko ezingaba abuye achube ukuqhubeka isimo sokugembula zingaveli isimiso sezinzwa esiyinhloko. A sebuningini odokotela bakholelwa ukuthi Rasmussen syndrome ibangelwa amasosha omzimba sokuhlasela kwamasosha omzimba, amagciwane kanye cytotoxic T-lymphocyte.

indima olungenzeka cytomegalovirus, okwakubekelwa behlukene cortex cerebral iziguli omdala. Kungenzeka ukuthi lezi Amagciwane abangela ukuvuvukala, zibe yesifo esingelapheki. Ngaphezu kwalokho, kungenziwa ukugqashuka yezinkinga yavela ngemva ukutheleleka ngaphambi.

Manje, ososayensi abaningi bakholelwa ukuthi kuyinto amasosha omzimba sokuhlasela kwamasosha omzimba imbangela encephalitis Rasmussen. Izimbangela zesifo is naye okusolakala zingachazwa ngezinqubo cytotoxic T-lymphocyte.

In iziguli Rasmussen Syndrome, ngezinye izikhathi atholakala phakathi kwezihlobo abaphethwe ezinye izifo sokuhlasela kwamasosha omzimba. Ngokwesibonelo, isifo Behçet sika. Lokhu kusikisela umbono wokuthi izihlobo zinengxenye inqubo sokugembula izici ezivamile zofuzo. Ikakhulu, okukhulunywe nezinto ezifana hla-galotipy.

Symptomatology entsifalita Rasmussen

Ekuqaleni, lesi sifo ububonisa ebalulekile motor nokuquleka. Njengoba isifo sihlasela ukuze ujoyine myoclonus wendawo. Ngokuhamba kwesikhathi, ukuhlasela kwaqina. Basuke ephelezelwa kwemisipha izinhlungu zibe, nokulahlekelwa ukwazi nokuwa. Ngokuvamile, iziguli sihlaselwa ngesikhathi sokulala.

Ukuthuthukela, lesi sifo kubonakala siphelelwe amandla ndikindiki ngokwengxenye okwenzeka nganoma iyiphi ingxenye yomzimba. Izifundo zikhombisa ukwehla kwezinga lomsebenzi ku-endaweni ethintekile ingqondo.

ukuhlola

Izimpawu liphinyiselwe kubantu abaphethwe i-unyaka syndrome ka Rasmussen. Encephalitis nge etiology ngokuzama ukubona kusenesikhathi. Lokhu kuvumela ukuba silangazelele nomphumela omuhle yokwelapha immunosuppressive. Ngakho kuqala kukho konke yakhetha ekutadisheni emitholampilo, i-MRI kanye Bheka wenziwa.

Izindlela nokwelashwa encephalitis Rasmussen sika

Ngoba kuze kube kukhona izingxabano ngezimbangela zokuziphendukela Rasmussen Syndrome, encephalitis ingelashwa nge izindlela ezivamile. Uma ukuthola zesifo anikeze isiguli imithi antiepileptic uhlamvu. Ncoma ukudla eklanyelwe ukwandisa ukusetshenziswa ukudla okunothe amafutha, kanye nokwehla inani ukudla Ukudla aqukethe carbohydrate. Ngokuvamile inosizo ukusebenzisa plasmapheresis, corticosteroids, immunoglobulin, ayisiza.

Ngokuvamile, ukwelapha isifo aye ayisebenzisa kaningi izindlela ezinkulu. Iziguli ephethwe isifo esingathí sina kodwa futhi eziyinkimbinkimbi okulimala ebuchosheni, kubalulekile ukwenza Ukufakelwa ka ezinzwa. Manje ngangokunokwenzeka sizama baqhube craniotomy.

Ngezinye izikhathi iziguli ahlinzekwa kokungenela kuhlinzwa - Hemispherectomy. Ngemva kube lula Rasmussen Syndrome. Encephalitis Yiqiniso, eshiya izibazi yayo, paresis noma nenkinga ngenkulumo evelele. Nokho, sihlasela nesineke mancane ezivamile.

Ukuze give up ukuhlinzwa akuyona kufiseleka, naphezu kweqiniso lokuthi zingaholeli ukuqedela ukuphulukiswa. Phela, ukuthuthukiswa sifo eshubisa eziphikelelayo kusilela esithinta izinzwa, ngokumelene lapho zikhona retardation engqondo nokukhubazeka.

Ezimweni izilonda zamazwe amabili ebuchosheni (zombili ama-) ukuqagela ngeshwa okungekuhle. Kuvulwe amacala amabili ekufeni phakathi kweziguli ezine-encephalitis Rasmussen evamile.