SikaLou Gehrig syndrome. Indlela yokubhekana nalesi sifo sikaCharcot?

SikaCharcot syndrome - kuyini nokuthi ukuze sibonakalise? Esisinikela yethulwa lesi sihloko.

Incazelo isifo

SikaCharcot Syndrome (noma claudication ngakanye) iyisifo libhekene ukubukeka kanye nekusita ubuhlungu futhi ubuthaka emikhawulweni ephansi ngesikhathi uhamba. ekhombisa okunjalo ngokuvamile kubangela isiguli ukuyeka, ngoba izimpawu wedwa okuthiwa cishe ungakhathazeki. Ngokuvamile lokhu ukwenqaba abantu bavezwa ngenxa:

• ngokweqile utshwala nokubhema;
• ukhuluphele;
• amazinga high blood cholesterol;
• ufuzo, nokunye.

Izimpawu main

SikaCharcot syndrome - lena ngempela yisimo esibuhlungu ebangela ubuhlungu nesineke futhi kakhulu kuthuntubeza ikhono lomuntu izinga lempilo. Nale ukwenqaba umuntu ngokuvamile ekhononda ukukhathala, kanye kabi ubuhlungu emilenzeni bezihambela, ikakhulukazi izibunu nemisipha ithole. Kukhona amacala lapho ubuhlungu ezindaweni ezithile emzimbeni imisipha emathangeni kanye okhalweni. Njengoba iziguli kwathiwa unesifo isifo sikaCharcot ngokwengxenye futhi sekubonakala buthaka ngokushesha ngemva ukuphumula emfushane.

Ngo leso sifo e emikhawulweni distal engezansi isiguli zivame waphawula iziyaluyalu trophic futhi vegetative-semithambo (isib, akrozianoz, izinyawo abandayo, marbling kwesikhumba kanye nezinguquko esiwohlozayo, ukungabi ishayela ku imithambo senyawo nezilonda ezingapholi neminwe, okuyinto ngokuvamile ubabonisa proximally isiqondiso).

Ngaphezu kwalokho, sikaLou Gehrig syndrome libhekene izinguquko esiwohlozayo futhi dystrophic e amathambo namalunga (hypertrophy izingxenye ngazinye, ukonakala kwazo uqwanga, ithambo yinkantolo Ukwemuka, osteophyte, waphuka intraarticular kanye nokuguqulwa lamathambo eside). Ngaphezu kwalokho, Ukunganaki futhi yehlise nozwela emalungeni kakhulu kwandisa ingozi yokulimala esibuhlungu.

izimbangela

SikaCharcot syndrome - isifo esibangelwa kokunqotshwa umlenze imithambo (thromboangiitis, obliterans isifo sokuqina kwemithambo yegazi, ifomu neuropathy ka aortoarteritis nonspecific nokunye.). Ubuhlungu nesineke zenzeka ngenxa enganele igazi ligeleze izicubu imisipha wemikhawulo aphansi. Futhi, lesi sifo kungase kubangelwe kokucindezelwa we equina iKhawuda e stenosis umgogodla, okungenani - ngenxa umgogodla intambo ischemia ku malformation arteriovenous, noma isifo sokuqina kwemithambo yegazi le-aorta.

ekwelapheni lesi sifo

Ukwelashwa Kweseva claudication liwumthombo oyinhloko ukwelashwa oqondile lesi sifo, okungukuthi imithambo. Ngokuvamile, izimo ezinjalo odokotela beluleka iziguli zabo ukuba alahle konke imikhuba emibi, unciphise umzimba futhi ukulandela ukudla okuqinile. Iziguli esabelwa futhi iqoqo olukhethekile umzimba, ukuthi uJesu Krestu, siyakumehlula izimpawu ezikhungathekisayo zalesi sifo.

Kepha izindlela olandelanayo ukwelashwa ngalesosikhathi they zibandakanya kokuthola imithi ehlukahlukene. Isenzo sabo kuqalisa analgesic kanye vasodilator. Futhi imali ekhemisi ukusiza ukwehlisa cholesterol egazini futhi dilution yayo.

Abadinga ahlekise kokungenela kuhlinzwa esetshenziswayo lapho inwebeka mafutha anciphisa isikhala esingaphakathi Umthambo ngokwethula kuwo ipayipi ekhethekile.

Syndrome, sikaCharcot-Marie-Izinyo isifo

Lokhu ukuphambuka limelela leqembu lezifo ngofuzo, izimpawu ukonakala kwazo neuropathy yezinzwa. Kufanele kuqashelwe ukuthi ezahlukeneyo ezahlukene ngokuthi syndrome kungenziwa okusekelwe obungefani zofuzo. Eziningi zalezi zifo zizuzwe i autosomal indlela evelele. Nokho, okwamanje eziveziwe embodiments izifo ezihambisana ne adhesion we-X chromosome.

Ngo kokutshelwa ngokukhubazeka kwengane, sikaCharcot-Marie syndrome, e isiguli abathintekayo umgogodla nezinzwa neuropathy. Kuye isici ngezakhi zofuzo kubantu zingase zimiswe peripheral axonal noma demyelinating.

Ngokuvamile lalimelela ukuphambuka ucala kutfutfukisa entsheni noma usakhula. Izimpawu leli qembu isifo ekugcineni wachaza, futhi isifo siqhubeka, lapho kwenzeka kwelizinga ukukhubazeka, hhayi esokufa.

Izimpawu ukungamukeleki

Lesi sifo iqala ukuphuma ngaphansi distal imisipha yoma ukuba buthakathaka kwezicubu umlenze. Ngokuhamba kwesikhathi, izinyawo sikhubazekile nezinzwane zinkulu futhi hammertoes. Ezinganeni nale Ihlahlubo cishe njalo kubonakala imisiwe ukuthuthukiswa ngokomzimba.

Ukwelashwa kwezifo lezinceku

ukwelashwa Specific kwesimiso sokugembula enjalo ayikho. Nokho, ukuthuthukisa impilo iziguli, odokotela bavame linqume Physiotherapy futhi ukwelashwa. Ngaphezu kwalokho, iziguli nale Ihlahlubo kabanzi zonke izinhlobo amadivaysi ezokwelapha evumela kuqede izimpawu ubuhlungu. Ngokwesibonelo, lapho unyawo ukulengiswa isicelo umkaki wamathambo yokugcizelela shank nokunye. Futhi-ke inenani elikhulu Ukwelulekwa zofuzo.

isifo Von Willebrand sika

Kufanele kuqashelwe ukuthi izifo lezinceku zihlanganisa hhayi sikaCharcot kuphela Syndrome. isifo Von Willebrand lingasetshenziswa futhi wadluliselwa eziseduze.

Njengoba yaziwa, ukuphambuka imelelwa iziyaluyalu ezivamile ngofuzo, okuholela ukuphazamiseka coagulation igazi noma inqubo ekunqandeni. Nokho, ngokuvamile isifo kwenzeka phakathi nenkambo yokuphila ngenxa ezinye izifo (ifomu ie atholwe).

izimpawu isifo

Ingozi ukopha lapho ukuphambuka enjalo yehluke kuye uhlobo isifo. Izici eziyinhloko lesi sifo sitholakala ngofuzo kukhona umongozima yansukuzonke, nokulimala oludlulele kanye nokulimala, nokopha izinsini, kanjalonjalo. Abesifazane kungenzeka ube nzima ukuya esikhathini, futhi ngesikhathi sokuzalwa ubungozi bokulahlekelwa esiningi igazi.

ekwelapheni lesi sifo

Iziguli nale Ihlahlubo akukho ukwelashwa kuyadingeka, kodwa ingozi ukopha kakhulu baye bagqugquzela njalo. Ngakho, isiguli kungenziwa Kunconywa izidakamizwa okuyinto ukunciphisa uphawu okucacile isifo. Uma isiguli kuhlelelwe ukwenza ukuhlinzwa, udokotela kufanele lokufeza ukwelashwa kokuvimbela.