Anaemia Sideroblastic: izimpawu, ukwelashwa

Abantu abaningi bayazi ukuthi anaemia iyisifo kuyingozi kakhulu. Kukhona izinhlobonhlobo eziningi zalesi sifo, futhi ngayinye kuwo kuyingozi empilweni yomuntu. anaemia Sideroblastic kuyinto zokugula esiyingozi elihlobene ne kahle microelements zamagama. Kulesi isifo kuyofika emnkantsheni ithambo usebenzisa nensimbi yokwensimbi-hemoglobin inhlangano, + ngakho-ke lifakwa izitho zangaphakathi. Into esemqoka - ukuvimbela izinkinga, kanye le njongo kufanele ngokushesha nokufuna usizo lochwepheshe.

Umcabango

anaemia Sideroblastic kuyehluka kuneminye izinhlobo zezifo encishisiwe lokuhlushwa yensimbi amangqamuzana abomvu. Iqiniso lokuthi kuyofika emnkantsheni ithambo akasebenzisi lesi sici ku synthesis elithwala umoya-mpilo. Ngokuvamile, ukugula buyaqina lapho azalwa naso noma bathenga. Ezingeni zofuzo, ukuntuleka kwegazi emzimbeni kwenzeka ikakhulu abafana.

Lesi sifo angadluliselwa njengenhlangano autosomal ngendlela evelele. Lokhu kubizwa ngokuthi i-anemiya syndrome Pearson. Lapho umzimba ayiqondakali amuncwa yensimbi, it is zibekwe izitho zangaphakathi, okuholela anaemia sideroblastic. Uma indlala kuba kakhulu, umsebenzi sinqamukile isibindi, izinso kanye senhliziyo esilimele.

izinhlobo izifo

Lolu hlobo lwe-anaemia lihlukaniswe by degree of kobukhulu, kodwa futhi ngenxa ukubukeka isithombe emtholampilo. Izinhlobo eziningana abahlukene igazi sideroblastic:

1. Ukubambezeleka. Lesi sifo kuthiwa ngofuzo ngenxa isakhi sofuzo wezakhi. Lokhu kubangela anomaly zokugula umzimba inqubo ezihilela B6 futhi aminolevulinic acid. Lesi sifo izenze wazizwa emva kokuzalwa noma phakathi nenkathi yokuqhuma kobusha.
2. Azalwa naso. Leli fomu isehlane eceleni, nakuba kwezinye ngokwezinga sihlobana ifomu sitholwa njengefa. Lapha, elinesimo wokuqukethwe lelisetulu erythrocyte coproporphyrin.
3. Ngazuza. Kubonakala ngenxa imiphumela emibi amakhemikhali. Phakathi kwabo kukhona Ethanol, okuhola tsiklosirin.

Izinkinga yensimbi zamagama futhi zenzeka ngenxa isimila izinqubo emzimbeni. Cishe 1/10 iziguli igazi sideroblastic uhlushwa wegazi oyingozi.

Izimbangela isifo

Imbangela eyinhloko isifo iyona protoporfiirina yokuntuleka, okuyinto ingenye yezingxenye ezibaluleke kakhulu synthesis-hemoglobin isici. Ngaphezu kwalokho, izinto ezihilelekile kudalwa amaprotheni ngaphezulu nensimbi.

kuphakama Kutholiwe ifomu anaemia sideroblastic kusukela lokuthi umzimba asisho ukungena izinto ezidingekayo imali eyanele. Kunezimo lapho kwakwakhe oyifunayo kuthiwa ukuyiveza ngemithi esithatha abantu.

Umzimba Akukho lutho olusele ngenxa yokuchayeka utshwala. Isifo sokulahlekelwa yigazi kungenzeka ngenxa ubuthi phambili noma reception kwamaphilisi eqinile. Ifomu lezinceku is badabula chromosome zesifazane ufuzo lilimele. Futhi, imbangela isifo kungenzeka ukuphazamiseka kwesimiso somzimba sokuzivikela ezifweni kanye nokuthuthukiswa izinqubo neoplastic.

Sifo anaemia sideroblastic

Yokukhomba lesi sifo ngempela eziyinkimbinkimbi, njengoba wabe cishe asymptomatic. Ngaphezu kwalokho, kukhona isithombe abahlukene zokwelapha, okuyinto ungathembela. Uma ubheka kuphela ngesikhathi izimpawu zangaphandle, sitholakele lesi sifo ngiyaphupha. Nokho, kukhona enye indlela ukuthola anaemia sideroblastic - ukuhlolwa igazi.

Bazijayeze Ukuhlola izibilini nesineke, ukuthola ezifakwa yensimbi. Kodwa yi-elementi isikhathi, futhi ngakho-ke ebangela izimpawu hematological. Ukuze ugweme amaphutha, kubalulekile ukuqinisekisa uphethwe. Lokhu kwenziwa ngosizo isifundo macroscopic we umnkantsha.

Ukuze ukuthi ingozi lincishisiwe, kubalulekile ukuqhuba biopsy. Kuyinto le nqubo kuyindlela ephumelela kunazo ukunquma anaemia sideroblastic. It Kwenziwa kanje: biopsy zangaphambi ibala esikhethekile, futhi uma yensimbi non-kwemiqondo itholiwe, compounds omele kuzobonakala.

Ukuze lokho isazi ukubhekana?

Njengoba sekuphawuliwe kakade, izimpawu igazi sideroblastic cishe kunqunywa. Isithombe emitholampilo naye olahlekile, futhi ngenxa ukuthi kukhona ubunzima obuthile. Uma umuntu enomuzwa ukukhathala, ubuthaka emzimbeni, ngokuvamile libhekisela owelapha. Udokotela for anaemia esolwa athumele isiguli ukuba eyisazi ngubani cwaningo.

Okokuqala, uchwepheshe uthola isimo jikelele isiguli unesithakazelo yokuphila, imikhuba emibi, uhlu izifo kanye t lihlehlisiwe. D. Uma udokotela njengoba libona kufanele, uyobe ubambe izifundo eziningana. Lezi zihlanganisa:

• igazi (kanye kwamakhemikhali);
• isibindi biopsy;
• ukuhlaziya umnkantsha cell kwengoma.

Hematologist kungaba optionally uqondise nesineke kwabanye ongoti kuhlolisiswe egcwele. Ngokwesibonelo, ukuze uthole ifomu igazi, kubalulekile ukuba siphendukele zofuzo. Lokhu udokotela eyonquma ukuthi kukhona ukuba ifomu lezinceku anaemia sideroblastic. Iphinde kungase kudingeke uxhumane udokotela wezifo zabesifazane, Urologist noma Proctologist.

Izindlela yokwelashwa

Ngaphambi kokuba uqale ukwelashwa, kumele anqume ukuthi bukhona ngempela yensimbi sebethule. Ngenxa yale njongo, desferalovuyu isampula. It iqondiswa ujove esicutshini, kanye umchamo kwaphumela kumele zabelwe cishe 0.5-1.1 mg zensimbi, ngesikhathi hypochromic, gipersideremicheskoy, sideroahrestical, anaemia sideroblastic - 5.10 mg.

Kuyaphawuleka ukuthi ifomu lezinceku isifo ngeke welaphe. Ukucindezela isakhi sofuzo esikhiqiza waqala liguquke ukwelashwa esetshenziswa njalo nge ebulilini B6. It is yaphathwa imali mg 100 ngosuku. Nokho, ukusabela komzimba cishe ezingalindelekile. Ekwelapheni sideroblastic anaemia-hemoglobin ezingeni kufanele ifike amazinga evamile kungakapheli izinyanga ezintathu. Uma ngalesi sikhathi kwesikhathi kungasizi, eminye yokwelapha engenamsebenzi.

Izinhlelo ezivimbayo futhi Izibikezelo

Kaningana, isifo kubangelwa ubuthi phambili. Ukuze uvimbele lokhu, ukunakekelwa kufanele kuthathwe ukubhekana nale ndaba. Phakathi kabusha izindlu ezindala kudingeka sithathe izinyathelo zokuphepha ngangokunokwenzeka ukuze yawoyise izingane okwesikhashana. Musa bachithe gqiba upende equkethe phambili. Kungcono ukuba kwesulwe noma uzisuse amakhemikhali. Ngaphezu kwalokho, isidingo ukuqapha njalo inhlanzeko kwezakhiwo, athobele wokwakha impilo amazinga.

Yelaphani ifomu lezinceku isifo akunakwenzeka. Ukuze kuqinisekiswe imiphumela ezuzisayo kudingeka sihlale njalo siqaphele ibala igazi, ikakhulukazi ezingeni elithwala umoya-mpilo. Lokhu ibangelwa ukudlula njalo inkambo yokwelapha, okuyinto akuvumeli isifo nomsebenzi walo wokusungula nokulondoloza isimo evamile yomuntu.