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Myasthenia gravis: kuyini? Izimbangela, Izimpawu kanye Ukwelashwa Izindlela

Myasthenia ngokuthi isifo okuyinto kuhambisana anda buthakathaka kwezicubu. Isifo esifanayo achazwa ngokokuqala 1672. Ngokwezibalo, lesi sifo lokhu kungenzeki kaningi kakhulu. Noma kunjalo, abantu abaningi banesithakazelo imibuzo mayelana nokuthi kungani kukhona owesilisa, kuyini futhi yini izimpawu ilandelwe. Phela, ekuhlonzweni kuncike lwemithi futhi izinga lempilo umuntu ogulayo.

Myasthenia gravis - kuyini? Izimbangela isifo

Uma konke kungokwemvelo, acetylcholine phezu excitation engena emfantwini izinhlaka zokuxhumana zobuchopho, okuyinto ethatha ku-receptor ethize ezicutshini ulwelwesi - ngaleyo ndlela ziyashukumiseka nokwehlisa imisipha zesivikelo sesifuba. Kodwa in izinsana, lokhu mshini ukudluliselwa ngiyibona emsipheni siphukile.

Ngokushesha kuyafaneleka ukuthi myasthenia gravis - isifo esidluliselwa ngofuzo. Futhi namhlanje isinqumo ukwaba amafomu ezimbili eziyisisekelo ngendlela. Kwezinye izimo, ukwahluleka ukudluliselwa nerve ngiyibona lihlotshaniswa ukuphazamiseka ukusebenza evamile hypothalamus. Enye imbangela ezivamile isifo kuyinto lesion sokuhlasela kwamasosha omzimba we ndlala thymus, okuholela ukuncipha lemali kwemiqondo acetylcholine.

Kukhona okuthiwa myasthenia ezisanda kubelethwa gravis. Kuyini lokhu? Le ndlela lesi sifo kwenzeka izinsana uma konina baphazamisekile ka conduction kwamanyuroni.

Izimpawu zesifo engaveza njengasezulwini emva kokuzalwa ngezinsuku zokuqala, futhi umuntu omdala ngaphezulu. Kunezici ezithile ingozi ukuthi angenza myasthenia ekuthuthukiseni gravis. Izizathu ukuhlaselwa ka buthakathaka kwezicubu kungaba ngenxa kwengcindezi enkulu ukucindezeleka kwemizwa, izifo ezithathelwanayo esidlule nokuphazamiseka kwesimiso somzimba sokuzivikela ezifweni.

Izimpawu eyinhloko myasthenia gravis

Njengoba sekushiwo, isici esiyinhloko lesi sifo ukuba buthakathaka kwezicubu. Ekuseni, iziguli Uvame ukuzizwa ngokuphelele evamile. Kodwa ngemva kwamahora ambalwa kamuva le imisipha yohlaka niphele ziyeke ukusebenza, kuze agcwalise ukukhubazeka. Ngemva kokuphumula ikhono ukunciphisa walulama.

Kuye iqembu abathintekayo nezinzwa ihlukaniswe izinhlobo ezintathu eziyinhloko zesifo:

  • Kaningi, lesi sifo sihlasela imisipha, okuyinto innervated ngu nezinzwa cranial. Futhi isici esiyinhloko kulokhu ptosis. Uma umuntu engase aphumule ngokuphelele vula amehlo akho, bese ngemuva kwamahora ambalwa, kukhona sawo kancane kancane Isivalo engenhla.
  • Kukhona bulbar myasthenia gravis. Kuyini lokhu? Lesi sifo kuhambisana esephule ukudluliswa emsipheni ngokubhuduzela ukuze imisipha, okuyinto banesibopho e ukugwinya, ukuhlafuna namanye izinqubo. Iziguli zabantu unezinkinga yokudla, kanye ushintsho kancane kancane izwi, kwaze kwaba yilapho zinyamalala wako.
  • Ngesimo generalized iningi isifo sitholakale, lapho izicubu iso iyathinteka kuqala, bese inqubo wabe entanyeni, emikhawulweni engenhla, nokunye. D.

Izindlela nokwelashwa myasthenia

Kuyaphawuleka ukuthi myasthenia isifo gravis kuyingozi kakhulu futhi kudinga bezokwelapha abanekhono. Iqiniso liwukuthi ukuthi lesi sifo libhekene nezinkinga okuthiwa, okuyinto ahambisana ukukhubazeka isikhashana imisipha zokuphefumula, futhi lokhu kuyinto usongo ngqo ukuphila.

Le nqubo yokwelapha ngempumelelo kuphela ekuphathweni izidakamizwa equkethe acetylcholinesterase - a "Proserpine" futhi "Kalimin". Ukwelapha okunjalo zokugcina iminyaka, futhi umthamo imithi kushintsha njalo kuye ngokuthi isimo futhi ulinganisele yentuthuko isifo. Uma myasthenia gravis athuthukile ngokumelene isizinda kuwuphawu lwesimila we ndlala thymus, ukuhlinzwa wenziwa ukususa umzimba.

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