Impilo, Izifo nemibandela
Hamartoma ka wamaphaphu: izimbangela, izimpawu, ukwelashwa
Hamartoma ka wamaphaphu presents ekhethekile dizembrionalnoe kumiswa ehlanganisa advantageously yezingxenye we bronchial odongeni wamaphaphu parenchyma. anomaly yaqale ezichazwe 1904.
Uhlolojikelele
Ngaphansi hamartoma kwakusho ukuthi unesimila ingozi yamaphaphu, elibandakanya uqwanga, imithambo yegazi kanye nesakhiwo fibrous. Pathology ngokuvamile isebenze ingaphakathi parenchyma wamaphaphu, ngenxa yobukhulu bawo amancane has cishe akunamthelela ukusebenza kwezitho.
Hamartoma simele kumiswa olulodwa oyisiyingi esingamakhilomitha ukuthungwa obukhulu, ubukhulu zazo kuyahlukahluka kusuka 0.5 kuya 5 cm. Anomaly ngokuvamile hhayi kuhluke ukuthambekela ukukhuphuka okuqhubekayo, kodwa zokwelapha amacala yokunquma ukuthambekela ukwenyuka kancane ubukhulu zokugula ezaziwayo. Phakathi kwabo bonke labo izimila wamaphaphu hamartomas ingozi yemvelo umbukiso ngokuvamile (60% amacala). Lesi sifo ikakhulukazi kutholakala kwabesilisa.
omsakazo
Lung hamartoma eba ngenxa yokwephula wokukhula kwengane esiswini namanje e -embryonic period. Siqukethe izinhlobo ezihlukahlukene zezindwangu ezingaba izakhi ezicutshini embryonic, futhi izingxenye ezifanayo ngokwemvelo zomzimba kuwo ngqo elise. Lena umehluko oyinhloko kusukela hamartomas teratoma. Lesi sakamuva ngokuvamile uhlanganisa umklamo nezicubu izakhi alien isitho lapho itholakala.
ngezigaba
Sekukonke kukhona ngeengaba eziningana lesi sifo. Ngokwe predominance of ingozi wamaphaphu isimila izicubu:
- Lipomatous.
- Organoid.
- Hondromatoznaya.
- Angiomatous.
- Leyomiomatoznaya.
Ngokuya ngenombolo izimila ukuhlukanisa olulodwa futhi ezahlukeneyo eziningi zokugula. Kwasendaweni ukukhululwa endobronchial, intrapulmonary subpleural nemfundo.
emitholampilo isithombe
Hamartoma ukukhanya isikhathi eside Asinakukubonisa izimpawu sici. Ukwakheka okuqhubekayo subpleural ngokuvamile uhambisana ubuhlungu ukungakhululeki endaweni esifubeni. Uma hamartoma kumiswa bronchus odongeni, njengoba zingaphazamisa permeability ze- bronchi. Kulokhu, iziguli esekhala ukukhwehlela ezinzima ngokuhlukaniselwa muco-ubovu isikhwehlela, ezimweni ezingajwayelekile kukhona hemoptysis.
uphethwe
Ngenxa yokuthi i-pathology kuyinto ogxile asymptomatic, kungenzeka ukuthola kuphela ngesikhathi sokuhlolwa isimiso. Ukuze udokotela emtholampilo olunemininingwane ethe xaxa sinquma luhlolo radiology, lapho Kutholwe emthunzini Umumo oyindilinga letingemasayizi lahlukene kanye wabuka ngqo noma mihlobiso. Ngokuvamile, ama-X-ray kunqunywa calcareous inclusions. Isibalo sabo ngenxa ukushuba izithunzi. Uma uchitha ucwaningo olwathatha isikhathi ashukumisayo, kungabonwa ukuthi ubukhulu hamartoma wamaphaphu siyashintsha kancane kakhulu. Ngakolunye uhlangothi, ukushuba ezifakwa lime uyathuthuka ngokushesha.
Ezemfundo imvelo endobronchial wabonakaliswa izimpawu nenkhulumombiko. Esimweni sokuqala-ke imayelana isimila eyindilinga nge imiphetho bushelelezi futhi abukhali, selitholakala ngu-X-ray. ukubonakaliswa ongaqondile - kuyinto atelectasis, hypoventilation, kanye nezinye izimpawu kwephulwe conductivity bronchial.
A indima ekhethekile kunikezwa uphethwe umehluko. Kubaluleke kakhulu hhayi ukudida lokhu zokugula we -peripheral umdlavuza wamaphaphu futhi tuberculoma.
Yini okufanele baphathwe?
Phakathi kokubonisana udokotela kufanele kuqala kunazo zonke ukusho ukuthi kuyinto hamartoma yamaphaphu, kubangela yesifo nayo ukwelashwa okufanele. ukwelashwa izidakamizwa, ngeshwa, ekulweni nalenkinga ayizwakali. imithi zithathwa kuphela ukunciphisa imiphumela yezimpawu.
Zonke iziguli nokuhlinzwa Kunconywa ngaphandle kokukhetha. Uma udokotela iye yaqinisekisa ukuxilongwa "hamartoma ka wamaphaphu", ukusebenza ubhekwa isilinganiso olungenamkhawulo. Uma usola i-pathology ethile (isibonelo, umdlavuza neuropathy) kubalulekile makudle thoracotomy.
Hamartoma isuswe ngu husking noma resection ka wamaphaphu izicubu. Ukusebenza kusetshenziswa nezikhamo msebenzi, okuthiwa ugwema sebeziqhumbuza esibuhlungu. Lapho Izimo isihlobo ukuba lolu hlobo uzongenela observation kuvunyelwe othakazelisayo nesiguli ezinyangeni ezimbalwa. Emva kwalesi sikhathi umbuzo ukuhlinzwa yanquma esekelwe khona noma ukungabi khona okwandisa umthunzi phezu radiograph.
Kudinga ukuhluka indlela hamartoma endobronchial. Ukwelashwa kulokhu kusho nokususwa imfundo bronhotomii resection noma isitho udonga.
ukuba nombono ongafani ngeke
Hamartoma ukhula kancane kakhulu, kodwa ungakwazi sewenziwa omkhulu. Ukuzalwa kabusha e umdlavuza salo ezingavamile kakhulu. Ngokwe ngolwazi lwezibalo atholakalayo, kungenzeka umdlavuza akuyona ezingaphezu kuka-7% kuzo zonke izimo. Umdlavuza zandise kuzo zombili ingxenye EPITHELIAL futhi mesenchymal kwetinhlavu, kulandele Ukudlulela ukuba izindlala zamanzi, isibindi kanye nomgogodla wesintu.
Sithemba ukuthi wonke ebhalwe kuloluGunyazo, ngale sihloko, ulwazi kuyoba ngawe empeleni abe wusizo. Hlala uphilile!
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